Cherubism
Kalıtsal - AD
İlk bulgular 2-5 yaşlarında
Çenelere (birinde/ikisinde) bilateral, simetrik genişleme
Altçenede koronoidlere ve kondillere dek etkilenme
Büyüyen üstçenenin göz kapaklarını aşağı çekmesi (cherubic look)
Azıların eksikliği
Dişlerin erken yitirilmesi (süt)
Maloklüzyon
Gingival fibromatozis
Puberteyle birlikte gerilemeye başlayan ağrısız oluşumlar
Radyolojide bilateral multiloküler litik lezyonlar
Mikroskopide dev hücreleri içeren fibroblastik aktivite
Submandibular lenfadenopati
Optik nöropati
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De Lange J, Van den Akker HP. Clinical and radiological features of central giant-cell lesions of the jaw. Oral Surgery, Oral Medicine, Oral Pathology, Oral Radiology, & Endodontology, 99:464–470, 2005
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Carvalho Silva E, Carvalho Silva GC, Vieira TC. Cherubism: clinicoradiographic features, treatment, and long-term follow-up of 8 cases. Journal of Oral & Maxillofacial Surgery, 65(3):517-522, 2007
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Roginsky VV, Ivanov AL, Ovtchinnikov A, Khonari RH. Familial cherubism: the experience of the Moscow central institute for stomatology and maxillo-facial surgery. International Journal of Oral & Maxillofacial Surgery, 38:218–223, 2009
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Haritha A, Jayakumar A. Syndromes as they relate to periodontal disease. Periodontology 2000, 56:65–86, 2011
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Dyasanoor S, Naik S. Clinicoradiologic features of cherubism: a case report and literatüre review. General Dentistry, 62(5):e12-15, 2014
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Tsodoulos S, Ilia A, Antoniades K, Angelopoulos C. Cherubism: a case report of a three-generation inheritance and literature review. Journal of Oral & Maxillofacial Surgery, 72(2):405.e1-9, 2014
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Jiao Y, Zhou M, Yang Y, Zhou J, Duan X. Cherubism misdiagnosed as giant cell tumor: a case report and review of the literature. International Journal of Clinical & Experimental Medicine, 8(3):4656-4663, 2015