Epidermolysis bullosa acquisita
Edinsel
Orta yaşlarda belirir
Kronik otoimmun hastalık
Neden: Tip VII kollagene karşı otoantikorlar
Deri kırılgan
Mukozalar kırılgan
En küçük travmalarda deri ve mukozaları etkileyen büller
Büllerin iyileşmesinde sikatris oluşumu
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Generalize tip
Kırmızı-kaşıntılı plaklar
Alevlenme atakları
Ölümcül olabilir
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Mukozalara özgü tip
Ağız mukozasında veziküller/büller
Veziküller/büller: özofagus, konjunktiva, rektum, vagina
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Kasperkiewicz M, Sadik CD, Bieber K, et al. Epidermolysis Bullosa Acquisita: from pathophysiology to novel therapeutic options. Journal of Investigative Dermatology, 136(1):24-33, 2016
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Kim M, Borradori L, Murrell DF. Autoimmune blistering diseases in the elderly: Clinical presentations and management. Drugs & Aging, 33(10):711-723, 2016
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Asfour L, Chong H, Mee J, et al. Epidermolysis Bullosa Acquisita (Brunsting-Perry Pemphigoid Variant) Localized to the face and diagnosed with antigen identification using skin deficient in Type VII Collagen. American Journal of Dermatopathology, 39(7):e90-e96, 2017
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Wick MR. Bullous, pseudobullous, & pustular dermatoses. Seminars in Diagnostic Pathology, 34(3):250-260, 2017
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Vorobyev A, Ludwig RJ, Schmidt E. Clinical features and diagnosis of epidermolysis bullosa acquisita. Expert Review of Clinical Immunology, 13(2):157-169, 2017