Gri plaket sendromu
Kalıtsal - AR
Trombosit olgunlaşma bozukluğu (makrotrombositopeni)
Trombositlerde alfa granüllerinin yetersizliği
Ekimozlar
Burun kanamaları
Dişeti kanamaları
Cerrahi girişimlerde aşırı kanamalar
Mens kanamalarına bağlı demir eksikliği anemisi
Kemik iliği fibrozisi (myelofibrozis)
Splenomegali
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Jantunen E, Hänninen A, Naukkarinen A, et al. Gray platelet syndrome with splenomegaly and signs of extramedullary hematopoiesis: a case report with review of the literature. American Journal of Hematology, 46(3):218-24, 1994
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Nurden AT, Nurden P. The gray platelet syndrome: clinical spectrum of the disease. Blood Reviews, 21(1):21-36, 2007
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Gunay-Aygun M, Zivony-Elboum Y, Gumruk F, et al. Gray platelet syndrome: natural history of a large patient cohort and locus assignment to chromosome 3p. Blood, 116: 4990-5001, 2010
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Di Paola J, Johnson J. Thrombocytopenias due to gray platelet syndrome or THC2 mutations. Seminars in Thrombosis & Hemostasis, 37(6):690-697, 2011
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Valera MC, Kemoun P, Cousty S, et al. Inherited platelet disorders and oral health. Journal of Oral Pathology & Medicine, 42(2):115-124, 2013
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Nurden AT, Nurden P. Inherited disorders of platelet function: selected updates. Journal of Thrombosis & Haemostasis, 13 Suppl 1:S2-9, 2015